Primary Ewing Sarcoma of the Kidney in a 54-Year-Old Male: A Rare Case Report

Ewing sarcomas/Primitive neuroectodermal tumors are aggressive tumors, typically seen in children and young adults. These tumors are of neuroectodermal origin and, also known as Ewing sarcoma family tumors. They are most commonly seen in the bones and soft tissues. Primary Ewing sarcoma of the kidney is rarely seen. It has nonspecific symptoms and imaging findings. Therefore, it is mostly diagnosed postoperatively. Its diagnosis is based on histological morphology, immunohistochemistry and, molecular genetic tests. A multi-modality treatment approach is very important. Here, we presented a male patient with primary Ewing sarcoma of the kidney, relatively in older age. A 54-year-old male patient admitted to the hospital with right flank pain and hematuria. He was operated successfully and than received adjuvant vincristine, doxorubicin, cyclophosphamide, and ifosfamide, etoposide chemotherapy regimens. No treatment-related toxicity was observed and the patient is still in remission. Despite using surgery and adjuvant chemotherapy in treatment, because of its rarity there was no randomized trial about kidney Ewing sarcomas. These rare tumors still need robust therapeutic treatment regimens.